Clinical Case of the Complete Form of Androgen Insensitivity Syndrome (AIS)
https://doi.org/10.23934/2223-9022-2023-12-2-327-332
Abstract
The article presents a clinical observation of an extremely rare in gynecological practice androgen insensitivity syndrome (AIS). The authors give data on the pathogenesis of the disease, modern classification and terminology of various forms of this pathology. The phenotypic manifestations of the disease, the results of clinical and instrumental studies and surgical treatment are described.
The results of the study show the possibility of clinical diagnosis of AIS and timely surgical treatment of patients with this pathology, due to the high risk of gonadal malignancy.
About the Authors
M. M. Damirov
N.V. Sklifosovsky Research Institute for Emergency Medicine
Russian Federation
Russian Federation
Mikhail M. Damirov - Professor, Doctor of Medical Sciences, Head, Department of Acute Gynecological Diseases, N.V. Sklifosovsky Research Institute for Emergency Medicine.
3, Bolshaya Sukharevskaya Sq., 129090, Moscow
I. V. Anchabadze
N.V. Sklifosovsky Research Institute for Emergency Medicine
Russian Federation
Russian Federation
Irina V. Anchabadze - Candidate of Medical Sciences, Senior Lecturer, Educational Department, N.V. Sklifosovsky Research Institute for Emergency Medicine.
3, Bolshaya Sukharevskaya Sq., 129090, Moscow
A. A. Medvedev
N.V. Sklifosovsky Research Institute for Emergency Medicine
Russian Federation
Russian Federation
Alexander A. Medvedev - Chief, Department of Acute Gynecological Diseases, N.V. Sklifosovsky Research Institute for Emergency Medicine.
3, Bolshaya Sukharevskaya Sq., 129090, Moscow
M. A. Eremenko
N.V. Sklifosovsky Research Institute for Emergency Medicine
Russian Federation
Russian Federation
Maria A. Eremenko - Clinical Intern, N.V. Sklifosovsky Research Institute for Emergency Medicine.
3, Bolshaya Sukharevskaya Sq., 129090, Moscow
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Review
For citations:
Damirov M.M., Anchabadze I.V., Medvedev A.A., Eremenko M.A. Clinical Case of the Complete Form of Androgen Insensitivity Syndrome (AIS). Russian Sklifosovsky Journal "Emergency Medical Care". 2023;12(2):327-332. https://doi.org/10.23934/2223-9022-2023-12-2-327-332
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