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<article article-type="research-article" dtd-version="1.3" xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance" xml:lang="ru"><front><journal-meta><journal-id journal-id-type="publisher-id">nmp</journal-id><journal-title-group><journal-title xml:lang="ru">Журнал им. Н.В. Склифосовского «Неотложная медицинская помощь»</journal-title><trans-title-group xml:lang="en"><trans-title>Russian Sklifosovsky Journal "Emergency Medical Care"</trans-title></trans-title-group></journal-title-group><issn pub-type="ppub">2223-9022</issn><issn pub-type="epub">2541-8017</issn><publisher><publisher-name>“N.V. Sklifosovsky Research Institute for Emergency Medicine”</publisher-name></publisher></journal-meta><article-meta><article-id pub-id-type="doi">10.23934/2223-9022-2025-14-1-203-215</article-id><article-id custom-type="elpub" pub-id-type="custom">nmp-2090</article-id><article-categories><subj-group subj-group-type="heading"><subject>Research Article</subject></subj-group><subj-group subj-group-type="section-heading" xml:lang="ru"><subject>КЛИНИЧЕСКИЕ НАБЛЮДЕНИЯ</subject></subj-group><subj-group subj-group-type="section-heading" xml:lang="en"><subject>CLINICAL OBSERVATIONS</subject></subj-group></article-categories><title-group><article-title>Комбинированное лечение гигантской экстра-интракраниальной артериовенозной мальформации</article-title><trans-title-group xml:lang="en"><trans-title>Combined Treatment of Giant Extra-Intracranial Arteriovenous Malformation</trans-title></trans-title-group></title-group><contrib-group><contrib contrib-type="author" corresp="yes"><contrib-id contrib-id-type="orcid">https://orcid.org/0000-0003-4518-9874</contrib-id><name-alternatives><name name-style="eastern" xml:lang="ru"><surname>Лукьянчиков</surname><given-names>В. А.</given-names></name><name name-style="western" xml:lang="en"><surname>Lukyanchikov</surname><given-names>V. A.</given-names></name></name-alternatives><bio xml:lang="ru"><p>Лукьянчиков Виктор Александрович - доктор медицинских наук, профессор кафедры фундаментальной нейрохирургии ФГАОУ ВО «РНИМУ им. Н.И. Пирогова» МЗ РФ (Пироговский Университет), ведущий научный сотрудник второго нейрохирургического отделения ФГБНУ «Научный центр неврологии», научный сотрудник отделения неотложной нейрохирургии ГБУЗ «НИИ СП им. Н.В. Склифосовского ДЗМ».</p><p>129090, Москва, Большая Сухаревская пл., д. 3; 117513, Москва, ул. Островитянова, д. 1</p></bio><bio xml:lang="en"><p>Viktor A. Lukyanchikov - Doctor of Medical Sciences, Professor of the Department of Fundamental Neurosurgery, N.I. Pirogov Russian National Research Medical University (Pirogov University); Leading Researcher of the Second Neurosurgical Department, Scientific Center of Neurology, Researcher of the Department of Emergency Neurosurgery, N.V. Sklifosovsky Research Institute for Emergency Medicine.</p><p>Bolshaya Sukharevskaya Sq. 3, Moscow, 129090; Ostrovityanova Str. 1, Moscow, 117513</p></bio><email xlink:type="simple">vik-luk@yandex.ru</email><xref ref-type="aff" rid="aff-1"/></contrib><contrib contrib-type="author" corresp="yes"><contrib-id contrib-id-type="orcid">https://orcid.org/0000-0002-5993-3310</contrib-id><name-alternatives><name name-style="eastern" xml:lang="ru"><surname>Далибалдян</surname><given-names>В. А.</given-names></name><name name-style="western" xml:lang="en"><surname>Dalibaldyan</surname><given-names>V. A.</given-names></name></name-alternatives><bio xml:lang="ru"><p>Далибалдян Ваган Ашикович - кандидат медицинских наук, врач-нейрохирург, старший научный сотрудник отделения неотложной нейрохирургии ГБУЗ «НИИ СП им. Н.В. Склифосовского ДЗМ».</p><p>129090, Москва, Большая Сухаревская пл., д. 3</p></bio><bio xml:lang="en"><p>Vagan A. Dalibaldyan - Candidate of Medical Sciences, Neurosurgeon, Senior Researcher of Department of Emergency Neurosurgery, N.V. Sklifosovsky Research Institute for Emergency Medicine.</p><p>Bolshaya Sukharevskaya Sq. 3, Moscow, 129090</p></bio><email xlink:type="simple">dalvahan@mail.ru</email><xref ref-type="aff" rid="aff-2"/></contrib><contrib contrib-type="author" corresp="yes"><contrib-id contrib-id-type="orcid">https://orcid.org/0000-0002-9660-3214</contrib-id><name-alternatives><name name-style="eastern" xml:lang="ru"><surname>Рощин</surname><given-names>С. Ю.</given-names></name><name name-style="western" xml:lang="en"><surname>Roschin</surname><given-names>S. Yu.</given-names></name></name-alternatives><bio xml:lang="ru"><p>Рощин Станислав Юрьевич - врач-нейрохирург, младший научный сотрудник отделения неотложной нейрохирургии ГБУЗ «НИИ СП им. Н.В. Склифосовского ДЗМ».</p><p>129090, Москва, Большая Сухаревская пл., д. 3</p></bio><bio xml:lang="en"><p>Stanislav Yu. Rosсhin - Neurosurgeon, Junior Researcher of the Department of Emergency Neurosurgery, N.V. Sklifosovsky Research Institute for Emergency Medicine.</p><p>Bolshaya Sukharevskaya Sq. 3, Moscow, 129090</p></bio><email xlink:type="simple">rochshinstas@gmail.com</email><xref ref-type="aff" rid="aff-2"/></contrib><contrib contrib-type="author" corresp="yes"><contrib-id contrib-id-type="orcid">https://orcid.org/0000-0002-5685-4916</contrib-id><name-alternatives><name name-style="eastern" xml:lang="ru"><surname>Гончарова</surname><given-names>И. И.</given-names></name><name name-style="western" xml:lang="en"><surname>Goncharova</surname><given-names>I. I.</given-names></name></name-alternatives><bio xml:lang="ru"><p>Гончарова Ирина Игоревна - кандидат медицинских наук, старший научный сотрудник отделения анестезиологии, врач анестезиолог-реаниматолог ГБУЗ «НИИ СП им. Н.В. Склифосовского ДЗМ».</p><p>129090, Москва, Большая Сухаревская пл., д. 3</p></bio><bio xml:lang="en"><p>Irina I. Goncharova - Candidate of Medical Sciences, Senior Researcher, Anesthesiology Department No. 1, Anesthesiologist-Resuscitator, N.V. Sklifosovsky Research Institute for Emergency Medicine.</p><p>Bolshaya Sukharevskaya Sq. 3, Moscow, 129090</p></bio><email xlink:type="simple">irishka_utkina@list.ru</email><xref ref-type="aff" rid="aff-2"/></contrib><contrib contrib-type="author" corresp="yes"><contrib-id contrib-id-type="orcid">https://orcid.org/0000-0001-8475-3410</contrib-id><name-alternatives><name name-style="eastern" xml:lang="ru"><surname>Гусейнова</surname><given-names>Г. К.</given-names></name><name name-style="western" xml:lang="en"><surname>Guseynova</surname><given-names>G. K.</given-names></name></name-alternatives><bio xml:lang="ru"><p>Гусейнова Гюльнара Кирам кызы - врач ультразвуковой диагностики, научный сотрудник отделения лучевой диагностики ГБУЗ «НИИ СП им. Н.В. Склифосовского ДЗМ».</p><p>129090, Москва, Большая Сухаревская пл., д. 3</p></bio><bio xml:lang="en"><p>Gyul’nara K. Guseynova - Ultrasound Diagnostics Doctor, Researcher at the Department of Radiation Diagnostics, N.V. Sklifosovsky Research Institute for Emergency Medicine.</p><p>Bolshaya Sukharevskaya Sq. 3, Moscow, 129090</p></bio><email xlink:type="simple">gyuli73@mail.ru</email><xref ref-type="aff" rid="aff-2"/></contrib><contrib contrib-type="author" corresp="yes"><contrib-id contrib-id-type="orcid">https://orcid.org/0000-0002-9992-9260</contrib-id><name-alternatives><name name-style="eastern" xml:lang="ru"><surname>Журавель</surname><given-names>С. В.</given-names></name><name name-style="western" xml:lang="en"><surname>Zhuravel</surname><given-names>S. V.</given-names></name></name-alternatives><bio xml:lang="ru"><p>Журавель Сергей Владимирович - доктор медицинских наук, заведующий научным отделением анестезиологии; врач анестезиолог-реаниматолог ГБУЗ «НИИ СП им. Н.В. Склифосовского ДЗМ».</p><p>129090, Москва, Большая Сухаревская пл., д. 3</p></bio><bio xml:lang="en"><p>Sergey V. Zhuravel - Doctor of Medical Sciences, Head of the Scientific Department of Anesthesiology No. 1, 3; Anesthesiologist-Resuscitator, N.V. Sklifosovsky Research Institute for Emergency Medicine.</p><p>Bolshaya Sukharevskaya Sq. 3, Moscow, 129090</p></bio><email xlink:type="simple">zhsergey5@gmail.com</email><xref ref-type="aff" rid="aff-2"/></contrib><contrib contrib-type="author" corresp="yes"><contrib-id contrib-id-type="orcid">https://orcid.org/0000-0003-0180-9154</contrib-id><name-alternatives><name name-style="eastern" xml:lang="ru"><surname>Каранадзе</surname><given-names>В. А.</given-names></name><name name-style="western" xml:lang="en"><surname>Karanadze</surname><given-names>V. A.</given-names></name></name-alternatives><bio xml:lang="ru"><p>Каранадзе Василий Амиранович - кандидат медицинских наук, заведующий нейрохирургическим отделением для лечения больных с сосудистыми заболеваниями головного мозга, научный сотрудник отделения неотложной нейрохирургии ГБУЗ «НИИ СП им. Н.В. Склифосовского ДЗМ».</p><p>129090, Москва, Большая Сухаревская пл., д. 3</p></bio><bio xml:lang="en"><p>Vasily A. Karanadze - Candidate of Medical Sciences, Head of the Department of Neurosurgery for the Treatment of Patients with Vascular Diseases of the Brain, Researcher of the Department of Department of Emergency Neurosurgery, N.V. Sklifosovsky Research Institute for Emergency Medicine.</p><p>Bolshaya Sukharevskaya Sq. 3, Moscow, 129090</p></bio><email xlink:type="simple">karanadzev@mail.ru</email><xref ref-type="aff" rid="aff-2"/></contrib><contrib contrib-type="author" corresp="yes"><contrib-id contrib-id-type="orcid">https://orcid.org/0009-0005-6686-3698</contrib-id><name-alternatives><name name-style="eastern" xml:lang="ru"><surname>Коблик</surname><given-names>А. С.</given-names></name><name name-style="western" xml:lang="en"><surname>Koblik</surname><given-names>A. S.</given-names></name></name-alternatives><bio xml:lang="ru"><p>Коблик Александра Сергеевна - врач по рентгенэндоваскулярным методам диагностики и лечения, младший научный сотрудник отделения рентгенохирургических методов диагностики и лечения ГБУЗ «НИИ СП им. Н.В. Склифосовского ДЗМ».</p><p>129090, Москва, Большая Сухаревская пл., д. 3</p></bio><bio xml:lang="en"><p>Aleksandra S. Koblik - Doctor of X-ray Endovascular Diagnostic and Treatment Methods, Junior Researcher, Department of X-ray Surgical Diagnostic and Treatment Methods, N.V. Sklifosovsky Research Institute for Emergency Medicine.</p><p>Bolshaya Sukharevskaya Sq. 3, Moscow, 129090</p></bio><email xlink:type="simple">aleksa373@mail.ru</email><xref ref-type="aff" rid="aff-2"/></contrib><contrib contrib-type="author" corresp="yes"><contrib-id contrib-id-type="orcid">https://orcid.org/0009-0003-1046-161X</contrib-id><name-alternatives><name name-style="eastern" xml:lang="ru"><surname>Рябухин</surname><given-names>В. Е.</given-names></name><name name-style="western" xml:lang="en"><surname>Ryabukhin</surname><given-names>V. E.</given-names></name></name-alternatives><bio xml:lang="ru"><p>Рябухин Виталий Евгеньевич - кандидат медицинских наук, старший научный сотрудник отделения рентгенохирургических методов диагностики и лечения, врач по рентгенэндоваскулярным диагностике и лечению ГБУЗ «НИИ СП им. Н.В. Склифосовского ДЗМ».</p><p>129090, Москва, Большая Сухаревская пл., д. 3</p></bio><bio xml:lang="en"><p>Vitaliy E. Ryabukhin - Candidate of Medical Sciences, Senior Researcher, Department of X-ray Surgical Diagnostic and Treatment Methods, Physician of X-ray Endovascular Diagnostics and Treatment, N.V. Sklifosovsky Research Institute for Emergency Medicine.</p><p>Bolshaya Sukharevskaya Sq. 3, Moscow, 129090</p></bio><email xlink:type="simple">Vitev71@bk.ru</email><xref ref-type="aff" rid="aff-2"/></contrib><contrib contrib-type="author" corresp="yes"><contrib-id contrib-id-type="orcid">https://orcid.org/0000-0003-3742-6374</contrib-id><name-alternatives><name name-style="eastern" xml:lang="ru"><surname>Сачков</surname><given-names>А. В.</given-names></name><name name-style="western" xml:lang="en"><surname>Sachkov</surname><given-names>A. V.</given-names></name></name-alternatives><bio xml:lang="ru"><p>Сачков Алексей Владимирович - кандидат медицинских наук, заведующий научным отделением острых термических поражений, врач-хирург ГБУЗ «НИИ СП им. Н.В. Склифосовского ДЗМ».</p><p>129090, Москва, Большая Сухаревская пл., д. 3</p></bio><bio xml:lang="en"><p>Aleksey V. Sachkov - Candidate of Medical Sciences, Head of the Scientific Department of Acute Thermal Injuries, Surgeon, N.V. Sklifosovsky Research Institute for Emergency Medicine.</p><p>Bolshaya Sukharevskaya Sq. 3, Moscow, 129090</p></bio><email xlink:type="simple">sachkovav@sklif.mos.ru</email><xref ref-type="aff" rid="aff-2"/></contrib><contrib contrib-type="author" corresp="yes"><contrib-id contrib-id-type="orcid">https://orcid.org/0000-0003-3515-8329</contrib-id><name-alternatives><name name-style="eastern" xml:lang="ru"><surname>Гринь</surname><given-names>А. А.</given-names></name><name name-style="western" xml:lang="en"><surname>Grin</surname><given-names>A. A.</given-names></name></name-alternatives><bio xml:lang="ru"><p>Гринь Андрей Анатольевич - член-корреспондент РАН, доктор медицинских наук, профессор кафедры фундаментальной нейрохирургии ФГАОУ ВО «РНИМУ им. Н.И. Пирогова» МЗ РФ (Пироговский Университет), заведующий научным отделением неотложной нейрохирургии ГБУЗ «НИИ СП им. Н.В. Склифосовского ДЗМ».</p><p>129090, Москва, Большая Сухаревская пл., д. 3; 117513, Москва, ул. Островитянова, д. 1</p></bio><bio xml:lang="en"><p>Andrey A. Grin - Corresponding Member of the RAS, Doctor of Medical Sciences, Professor of the Department of Fundamental Neurosurgery, Pirogov Russian National Research Medical University (Pirogov University), Head of the Scientific Department of Emergency Neurosurgery, N.V. Sklifosovsky Research Institute for Emergency Medicine.</p><p>Bolshaya Sukharevskaya Sq. 3, Moscow, 129090; Ostrovityanova Str. 1, Moscow, 117513</p></bio><email xlink:type="simple">aagreen@yandex.ru</email><xref ref-type="aff" rid="aff-1"/></contrib><contrib contrib-type="author" corresp="yes"><contrib-id contrib-id-type="orcid">https://orcid.org/0000-0001-5256-0905</contrib-id><name-alternatives><name name-style="eastern" xml:lang="ru"><surname>Крылов</surname><given-names>В. В.</given-names></name><name name-style="western" xml:lang="en"><surname>Krylov</surname><given-names>V. V.</given-names></name></name-alternatives><bio xml:lang="ru"><p>Крылов Владимир Викторович - академик РАН, доктор медицинских наук, профессор, заведующий кафедрой фундаментальной нейрохирургии ФГАОУ ВО «РНИМУ им. Н.И. Пирогова» МЗ РФ (Пироговский Университет), главный научный сотрудник отделения неотложной нейрохирургии ГБУЗ «НИИ СП им. Н.В. Склифосовского ДЗМ».</p><p>129090, Москва, Большая Сухаревская пл., д. 3; 117513, Москва, ул. Островитянова, д. 1</p></bio><bio xml:lang="en"><p>Vladimir V. Krylov - Academician of the Russian Academy of Sciences, Doctor of Medical Sciences, Professor, Head of the Department of Fundamental Neurosurgery, Pirogov Russian National Research Medical University (Pirogov University); Chief Researcher, Department of Emergency Neurosurgery, N.V. Sklifosovsky Research Institute for Emergency Medicine.</p><p>Bolshaya Sukharevskaya Sq. 3, Moscow, 129090; Ostrovityanova Str. 1, Moscow, 117513</p></bio><email xlink:type="simple">krylovVV@sklif.mos.ru</email><xref ref-type="aff" rid="aff-1"/></contrib></contrib-group><aff-alternatives id="aff-1"><aff xml:lang="ru">ГБУЗ «Научно-исследовательский институт скорой помощи им. Н.В. Склифосовского ДЗМ»; ФГАОУ ВО «Российский национальный исследовательский медицинский университет им. Н.И. Пирогова» МЗ РФ (Пироговский Университет)<country>Россия</country></aff><aff xml:lang="en">N.V. Sklifosovsky Research Institute of Emergency Medicine; N.I. Pirogov Russian National Research Medical University (Pirogov University)<country>Russian Federation</country></aff></aff-alternatives><aff-alternatives id="aff-2"><aff xml:lang="ru">ГБУЗ «Научно-исследовательский институт скорой помощи им. Н.В. Склифосовского ДЗМ»<country>Россия</country></aff><aff xml:lang="en">N.V. Sklifosovsky Research Institute of Emergency Medicine<country>Russian Federation</country></aff></aff-alternatives><pub-date pub-type="collection"><year>2025</year></pub-date><pub-date pub-type="epub"><day>16</day><month>04</month><year>2025</year></pub-date><volume>14</volume><issue>1</issue><fpage>203</fpage><lpage>215</lpage><permissions><copyright-statement>Copyright &amp;#x00A9; Лукьянчиков В.А., Далибалдян В.А., Рощин С.Ю., Гончарова И.И., Гусейнова Г.К., Журавель С.В., Каранадзе В.А., Коблик А.С., Рябухин В.Е., Сачков А.В., Гринь А.А., Крылов В.В., 2025</copyright-statement><copyright-year>2025</copyright-year><copyright-holder xml:lang="ru">Лукьянчиков В.А., Далибалдян В.А., Рощин С.Ю., Гончарова И.И., Гусейнова Г.К., Журавель С.В., Каранадзе В.А., Коблик А.С., Рябухин В.Е., Сачков А.В., Гринь А.А., Крылов В.В.</copyright-holder><copyright-holder xml:lang="en">Lukyanchikov V.A., Dalibaldyan V.A., Roschin S.Y., Goncharova I.I., Guseynova G.K., Zhuravel S.V., Karanadze V.A., Koblik A.S., Ryabukhin V.E., Sachkov A.V., Grin A.A., Krylov V.V.</copyright-holder><license license-type="creative-commons-attribution" xlink:href="https://creativecommons.org/licenses/by/4.0/" xlink:type="simple"><license-p>This work is licensed under a Creative Commons Attribution 4.0 License.</license-p></license></permissions><self-uri xlink:href="https://www.jnmp.ru/jour/article/view/2090">https://www.jnmp.ru/jour/article/view/2090</self-uri><abstract><p>Артериовенозные мальформации — это образования, состоящие из диспластических, расширенных кровеносных сосудов, в которых кровь, минуя капиллярную сеть, попадает в венозное русло и вызывает значительное расширение вен. Кроме того, артериовенозная мальформация может вызывать нарушения питания (трофики) мягких тканей, расположенных рядом с ними. Экстракраниальные артериовенозные мальформации представляют собой редкие и опасные сосудистые аномалии. На данный момент не существует универсальных алгоритмов их лечения. В этой статье представлен опыт хирургического комбинированного лечения пациента с экстракраниальной артериовенозной мальформацией. Сначала была проведена этапная эндоваскулярная окклюзия образования, а затем его полное удаление в условиях гибридной операционной. Такой подход позволил выполнить радикальное вмешательство с положительным результатом.</p></abstract><trans-abstract xml:lang="en"><p>Arteriovenous malformations are formations consisting of dysplastic, dilated blood vessels in which blood, bypassing the capillary network, enters the venous bed and causes significant expansion of the veins. In addition, arteriovenous malformations can cause nutritional disorders (trophism) of the soft tissues located near them. Extracranial arteriovenous malformations are rare and dangerous vascular anomalies. At present, there are no universal algorithms for their treatment. This article presents the experience of surgical combined treatment of a patient with extracranial arteriovenous malformation. First, staged endovascular occlusion of the formation was performed , and then its complete removal in a hybrid operating room. This approach allowed performing a radical intervention with a positive result.</p></trans-abstract><kwd-group xml:lang="ru"><kwd>артериовенозная мальформация</kwd><kwd>экстракраниальная мальформация</kwd><kwd>гибридная операционная</kwd><kwd>комбинированное лечение АВМ</kwd></kwd-group><kwd-group xml:lang="en"><kwd>arteriovenous malformation</kwd><kwd>extracranial malformation</kwd><kwd>hybrid surgery</kwd><kwd>combined treatment of AVM</kwd></kwd-group></article-meta></front><back><ref-list><title>References</title><ref id="cit1"><label>1</label><citation-alternatives><mixed-citation xml:lang="ru">Liu AS, Mulliken JB, Zurakowski D, Fishman SJ, Greene AK. Extracranial arteriovenous malformations: natural progression and recurrence after treatment. Plast Reconstr Surg. 2010;125(4):1185–1194. PMID: 20335868 https://doi.org/10.1097/PRS.0b013e3181d18070</mixed-citation><mixed-citation xml:lang="en">Liu AS, Mulliken JB, Zurakowski D, Fishman SJ, Greene AK. 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